TY  -  JOUR 
TI  - Combination of Hypertrophic Pachymeningitis, PR3-ANCA-positive Vasculitis, and Relapsing Polychondritis
PB  - J Rheumatol Publ Co
PY  - 2011
issn 0315-162X
AB  - Relapsing polychondritis (RP) is a rare connective tissue disease characterized by inflammation and destruction of cartilaginous tissue1. Although the exact underlying pathologic mechanism is unknown, it is widely accepted that there is a role of an autoimmune response in most cases2. Patients may have lung, renal, ocular, joint, and vascular compromise. Central nervous system (CNS) involvement is rare, and few cases have been described. We describe 3 patients with RP and CNS involvement manifested as hypertrophic pachymeningitis (HP), an inflammatory process that thickens the dura mater.
KW  - Ciencias socio biomédicas
KW  - Medical sciences
KW  - Ciclofosfamida
KW  - Policondritis
KW  - Enfermedades raras
KW  - Sistema nervioso central - Enfermedades
UR  - http://hdl.handle.net/10906/81192
ER  -